phone icon
+44 (0)1223 298875

Anti-CTSA Antibody

file icon Datasheet
ABclonal
A10884
Overview
Name: Anti-CTSA Antibody
Description: Rabbit polyclonal antibody to CTSA.
Applications: WB, IHC
Dilutions: WB 1:500 - 1:1000, IHC 1:20 - 1:50
Reactivity: Human
Immunogen: A synthetic peptide of human CTSA
Protein Length: 480
Host: Rabbit
Clonality: Polyclonal
Isotype: IgG
Purification: Affinity purification
Formulation: PBS with 0.02% sodium azide, 50% glycerol, pH7.3.
Storage: Store at 4℃. Avoid freeze / thaw cycles.

Target (Information from UniProt)
Function: Protective protein appears to be essential for both the activity of beta-galactosidase and neuraminidase, it associates with these enzymes and exerts a protective function necessary for their stability and activity. This protein is also a carboxypeptidase and can deamidate tachykinins.
Involvement in Disease: Galactosialidosis: A lysosomal storage disease associated with a combined deficiency of beta-galactosidase and neuraminidase, secondary to a defect in cathepsin A. All patients have clinical manifestations typical of a lysosomal disorder, such as coarse facies, cherry red spots, vertebral changes, foam cells in the bone marrow, and vacuolated lymphocytes. Three phenotypic subtypes are recognized. The early infantile form is associated with fetal hydrops, edema, ascites, visceromegaly, skeletal dysplasia, and early death. The late infantile type is characterized by hepatosplenomegaly, growth retardation, cardiac involvement, and a normal or mildly affected mental state. The juvenile/adult form is characterized by myoclonus, ataxia, angiokeratoma, mental retardation, neurologic deterioration, absence of visceromegaly, and long survival.
Sequence Similarities: Belongs to the peptidase S10 family.
Cellular Location: Lysosome.
UniProt: P10619
Gene ID: 5476
Synonyms: beta galactosidase 2 Antibody
BETA GALACTOSIDASE PROTECTIVE PROTEIN Antibody
beta-galactosidase 2 Antibody
beta-galactosidase protective protein Antibody
betagalactosidase 2 Antibody
Carboxypeptidase C Antibody
Carboxypeptidase L Antibody
carboxypeptidase Y-like kininase Antibody
Cathepsin A Antibody
deamidase Antibody
EC 3.4.16.5 Antibody
Glactosialidosis Antibody
GLB2 Antibody
Goldberg Syndrome Antibody
GSL Antibody
lysosomal carboxypeptidase A Antibody
Lysosomal protective protein Antibody
Lysosomal protective protein 20 kDa chain Antibody
Lysosomal protective protein deficiency Antibody
NEURAMINIDASE BETA GALACTOSIDASE EXPRESSION; NGBE Antibody
Neuraminidase deficiency with beta-galactosidase deficiency Antibody
NGBE Antibody
OTTHUMP00000031778 Antibody
OTTHUMP00000031781 Antibody
PPCA Antibody
PPCA deficiency Antibody
PPGB Antibody
PPGB_HUMAN Antibody
Protective protein cathepsin A Antibody
Protective protein for beta galactosidase Antibody
Protective protein for beta-galactosidase Antibody
Protective protein/Cathepsin A (PPCA) Antibody
Protective protein/cathepsin A deficiency Antibody
urinary kininase Antibody

Product Code - A10884
Size Price Quantity
100µl £243
200µl £372

or
Request a quotation
Contact us directly to order
  • call icon +44 (0)1223 298875
  • +44 (0)1223 281447
  • email icon orders@ab-y-ss.com
Product Quality
  • guarantee icon
  • We promise guaranteed product quality
  • and expert customer service.
Shipping Information
  • £20 to United Kingdom
  • £35 to Europe